Arch Dis Child 1994 Nov;71(5):450-1

Glycogenosis type IV: liver transplant at 12 years

Dhawan A, Tan KC, Portmann B, Mowat AP
Department of Child Health, King's College Hospital, Denmark Hill, London.

Abstract
Hepatomegaly, the presenting feature of type IV glycogen storage disease at 20
months of age, regressed during childhood. The patient remained asymptomatic
until 12 years of age when, after an episode of shock, septicaemia, and
spontaneous peritonitis, liver transplantation was successfully performed